Our search covered papers from 1972-2017 from different sources. Many rare diseases have limited information. Symptoms *. Specialists *. Its radiological appearance is of a "soap bubble" or "tennis racquet strings" [ 24 ]. Odontogenic myxoma can be found most often in young adults aged 25-35 years although lesions may occur over a lifetime, reporting the lowest . Odontogenic myxoma is an uncommon benign tumor that mainly affects the mandible, with a peak incidence in the second to fourth decades of life and predilection for the female sex. Recurrence rate ~25% Terminology Odontogenic myxoma Odontogenic myxofibroma Odontogenic fibromyxoma Epidemiology Most cases diagnosed in 2nd - 4th decades but wide age range of occurrence (between 1 to 73 years) More common in women Sites More common in mandible than maxilla 2/3 in mandible Clinical features Odontogenic myxomas are rare tumours that involve the mandible or maxilla and account for 3-6% of odontogenic tumours 2. Our aim was to establish the recurrence rate of odontogenic myxoma after different treatments. Odontogenic myxomas are categorized by the modified WHO classification under odontogenic ectomesenchyme with or without included odontogenic epithelium. OM is an odontogenic mesenchymal neoplasm. The papers were evaluated and critically appraised by two independent investigators. . We review the literature on the features, differential diagnosis, and treatment modalities of this lesion. Clinically, it is a slow-growing, expansile, painless, non-metastasizing, central tumor of jaws, chiefly the mandible. Radiographic features Odontogenic myxoma is considered a mesenchymal local aggressive, slow-growing, odontogenic tumour with well-defined pathologic characteristics and may be associated with tooth germ. The diagnosis poses a challenge because its clinical features overlap with those of other benign and malignant neoplasms. The greater variability in the clinical and radiological features of odontogenic myxoma emphasizes that it should be considered in differential diagnosis of both radiolucent and radiopaque lesions in both jaws. It rarely occurs in any bone other than jaws and peripherally. Context.Odontogenic myxoma is an uncommon tumor that has the potential for extensive destruction of the jaws.Objective.To document the clinical, pathologic, and behavioral features of odontogenic myxomas.Design.Histologic and immunocytochemical examinations were performed on odontogenic myxomas from 25 Chinese patients. What Information Does GARD Have For This Disease? Odontogenic myxoma Definition: Odontogenic myxoma is a rare, benign intraosseous tumor. Pathology Arises from mesenchymal odontogenic tissue. Objective Odontogenic myxoma is a rare intraosseous neoplasm, which is benign but locally aggressive. Abstract. Clinically, POM is presented as exophytic slowly growing mass which can be sessile or pedunculated. They are usually not painful. Odontogenic myxomas are benign but locally aggressive neoplasms found almost exclusively in the jaws and arise only occasionally in other bones. Genetic Testing *. Although enucleation and curettage have proven effective, the risk of recurrence remains considerable and long-term follow-up is indispensable. Odontogenic myxoma (OM) is a benign, but infiltrative tumor with mesenchymal cell origin. Introduction. Odontogenic myxoma (OM) is a benign intraosseous tumor, but locally invasive, having a high rate of recurrence. Odontogenic myxoma (OM) is a rare neoplasm, which originates from odontogenic ectomesenchyme. Introduction There is a network of reticulin fibres in this expanse of mucin. We present a rare case of odontogenic myxoma occurring in the mandible of a 19-year-old male patient with a brief review of clinical and radiological features, and diagnostic and operative . . We describe the case of a 13-year-old boy who developed recurrence of an odontogenic myxoma of the mandible. Symptoms Onset *. 1,2 OM is frequently reported to be the fourth or third most frequent odontogenic . Although peripheral odontogenic myxoma is a rare tumor, recent case reports are increasing. 2 according to some studies it is the second most-common benign odontogenic tumour, 3 is commonly seen in the Clinical and available follow-up data were analyzed . It preferably locates in posterior mandibular regions, followed by the incisors, maxillary and; exceptionally, the mandibular condyle. Our search covered papers from 1972-2017 from different sources. odontogenic myxoma is an uncommon benign odontogenic tumour that derives from mesenchyme, or odontogenic ectomesenchyme, or both, with or without epithelium.1 it comprises 0.5% of all bony tumours and 3%-6% of odontogenic tumours. Odontogenic myxoma (OM) is a benign neoplasm of ectomesenchymal origin with aggressive, potentially infiltrative, behaviour and is further defined as "an intraosseous neoplasm characterized by stellate and spindle-shaped cells embedded in an abundant myxoid or mucoid extracellular matrix". Though it has slight histologic overlap with other entities, definitive diagnosis is imperative considering the tumor's aggressive nature, high recurrence rate, and necessity of radical surgical intervention in large-sized lesions. 1. A myxoma is an uncommon connective tissue tumour consisting of scattered stellate cells spread in connective tissue mucin. The rate of recurrence decreased from 24.0% to 8.3% when follow-up exceeded 60 months. It is non-encapsulated, arises from odontogenic ectomesenchyme, develops solely in the jaws, and represent a small percentage of odontogenic tumor overall. Clinical, radiological, and histopathological features should be considered when making a diagnosis. Odontogenic myxoma is a slow growing benign, locally malignant tumour, notorious for recurrence. More evidence of long-term outcomes after conservative surgery for OM is needed. These lesions share clinical and histopathological features with many odontogenic tumors . We present a classical case of. Although surgery is usually the choice treatment, there is still some controversy concerning surgical techniques and proper indications. Cause *. The odontogenic myxoma is an uncommon benign odontogenic tumor arising from embryonic connective tissue associated with tooth formation. Odontogenic myxoma is a benign but locally aggressive intraosseous lesion of the jaws. Local recurrence can is possible. The recurrence rate and 95% CI were calculated in relat [1] As a myxoma, this tumor consists mainly of spindle shaped cells and scattered collagen fibers distributed through a loose, mucoid material. [2] Contents 1 Signs and symptoms 2 Diagnosis 3 Treatment It is characterized by excessive amount of mucoid ground substance. Our aim was to establish the recurrence rate of odontogenic myxoma after different treatments. It rarely appears in any bone other than the jaws. Abstract. Odontogenic myxomas are rare tumors that involve the mandible or maxilla and account for 3-6% of odontogenic tumors 2. There is no study in the literature that analyses the best standards for OM diagnosis and how the treatment modalities may influence the recurrence rates. The recurrence rate and 95% CI were calculated in relation to each specific treatment, and the chi . OM can be central (COM) or peripheral (POM) with the latter being rare and less aggressive. Odontogenic myxoma (OM) is an uncommon benign odontogenic tumor arising in the jaw. Abstract. The papers were evaluated and critically appraised by two independent investigators. Epidemiology Typically seen in the 2 nd to 3 rd decades of life (slightly earlier than ameloblastomas). Currently GARD is able to provide the following information for this disease: Population Estimate *. Odontogenic myxoma (OM) is an uncommon benign odontogenic tumor arising from the jaw bone. Last revised by Dr Yuranga Weerakkody . 2. It is considered to be derived from the mesenchymal portion of the tooth germ. Odontogenic myxoma is a benign but invasive tumor that has a high rate of recurrence after surgical removal ( Speight, 2013 ). Odontogenic myxoma is generally regarded as a rare benign tumor that occurs in tooth-bearing areas of the mandible and maxilla, and is characterized by its slow growth and bony invasions, resulting in painless facial deformity. Odontogenic myxoma represents less than 10% of all odontogenic tumours [ 8, 9 ]. Treatment 1..Radical surgery -Should be carried out in the hope of preventing recurrence . Odontogenic myxoma. 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